一例富含血供的咽旁非典型孤立性纤维性肿瘤并文献复习

Hypervascular atypical solitary fibrous tumor of parapharyngeal: a case report and literature review

摘要:

【】目的 探讨咽旁原发孤立性纤维瘤(Solitary fibrous tumor,SFT)的临床表现、影像表现、病理特征及鉴别诊断。方法 回顾性分析1例原发于咽旁、血供丰富(被外科误诊为海绵状血管瘤)的SFT,探讨其临床表现、影像表现及预后。结果 该病例的临床表现为局部无痛性肿物及压迫咽腔、气道引起相应症状,影像表现为占位性病变、且血供丰富,病理诊断为非典型孤立性纤维瘤,手术完整切除后随访4年未见复发。结论 咽旁的原发性SFT较为少见,易漏诊误诊,诊断需结合其临床表现、影像学检查,确诊有赖于病理检查。

关键词:咽旁间隙、孤立性纤维瘤、文献复习

Abstract:

【】Objective? To investigate the clinical manifestations, imaging features, pathological features and differential diagnosis of primary Solitary fibrous tumor (SFT) of parapharyngeal. Method A patient with parapharyngeal SFT with abundant blood supply and misdiagnosed as cavernous hemangioma by vascular interventional department was retrospectively analyzed to investigate its clinical manifestations, imaging manifestations and prognosis. Result The clinical manifestations of this case were local painless masses and compression of the pharyngeal cavity and airway causing corresponding symptoms, imaging manifestations were space-occupying lesions with rich blood supply, and pathological diagnosis was atypical solitary fibroma. No recurrence was found in 4 years of follow-up after complete surgical resection. Conclusion Primary parapharyngeal SFT is rare and easy to be missed and misdiagnosed. The diagnosis should be combined with clinical manifestations and imaging examination, and the diagnosis depends on pathological examination.

Key words:parapharyngeal, solitary fibrous tumor, literature review