Abstract:Relapsing Polychondritis(RP) is a rare immune multisystem disease mainly involve cartilage and protein-polysaccharide-rich tissues. Clinical manifestations of RP are greatly different due to the different involved tissues. There is still no specific auxiliary examination to be used as a means of effective diagnosis, which makes clinical diagnosis difficult. Patients with airway involvement can be hidden onset, who are easy to misdiagnosis and missed diagnosis due to atypical symptoms. However, the disease progresses quickly when the airway is involved. The treatment of late laryngotracheal stenosis is quite difficult and the prognosis is poor, which brings greater challenges to airway management. Therefore, clinicians should identify and improve the early diagnosis rate of RP patients with airway involvement as much as possible, and take not only systemic treatment, but also local treatment to manage the airway. This article reviews the progress of diagnosis and treatment of Relapsing Polychondritis with airway involvement to provide reference for clinicians.
