Abstract:ObjectiveExternal auditory canal cholesteatoma (EACC) is an uncommon disease of otorhinolaryngology. Early EACC lesions are not typical. Although EACC are benign tumors, they are biologically erosive. Early diagnosis and treatment of EACC are very important. Due to the relatively low incidence of EACC, there is no unified international standard for classification and staging of EACC. The treatment options of EACC mainly include conservative methods and surgical cleaning of cholesteatoma lesions. Therefore, more data need to be collected for a further comprehensive study. This paper systematically reviews relevant domestic and foreign literature, which summarizes and analyzes the etiology, pathogenesis and clinical characteristics of EACC in detail. This article will provide some help to arouse the attention of clinical otologists.